Hypoplastic left heart syndrome (HLHS) is a rare but severe congenital heart defect characterized by underdevelopment of left-sided heart structures, including the left ventricle, aortic valve, mitral valve, and ascending aorta. This condition leads to critically impaired systemic circulation, necessitating a patent ductus arteriosus for survival in the immediate neonatal period. Diagnosis often occurs prenatally through fetal echocardiography, with postnatal clinical findings including cyanosis, weak pulses, and signs of low cardiac output as the ductus closes. Management requires a staged surgical approach, including the Norwood, Glenn, and Fontan procedures, to establish single-ventricle physiology compatible with life. Despite advancements in care, HLHS patients face significant risks of morbidity and mortality, including heart failure, arrhythmias, and thromboembolic events, with long-term survival dependent on specialized medical and surgical interventions. This course provides clinicians with a comprehensive understanding of HLHS, from its pathophysiology and diagnostic approach to the intricacies of surgical management and long-term care. Participants gain insights into optimizing perioperative hemodynamics, managing complications of staged palliation, and addressing long-term issues such as Fontan physiology failure and associated comorbidities. Additionally, the course highlights the importance of interdisciplinary collaboration and patient-family education in improving outcomes. Clinicians emerge with enhanced clinical competence and confidence to care for patients with HLHS across the lifespan, contributing to improved survival rates and quality of life for this complex population.
Credit & MOC Details
Credit information is provided by the course provider. We recommend confirming credit eligibility with the provider or your licensing board before starting the activity.
Credit types
MOC types
FDA REMS
Qualifies for MIPS
Target Specialties
Relevant across 9 specialties.
Specialties served/covered
- Addiction Medicine
- Adolescent Medicine
- Advanced Heart Failure & Transplant Cardiology
- Allergy & Clinical Immunology
- Anatomic & Clinical Pathology
- Blood Banking & Transfusion Medicine
- Brain Injury Rehabilitation
- Breast Imaging
- Cardiac Anesthesia
- Cardiothoracic Surgery
- Cardiovascular Disease
- Chemical Pathology
- Clinical Cardiac Electrophysiology
- Clinical Informatics
- Critical Care Medicine
- Cytopathology
- Dermatopathology
- Diagnostic Radiology
- Endocrinology, Diabetes & Metabolism
- Facial Plastic & Reconstructive Surgery
- Foot & Ankle Surgery
- Forensic Pathology
- Gastroenterology
- General Internal Medicine
- General Operative Anesthesia
- General Otolaryngology
- General Pediatrics
- General Surgery
- Geriatric Medicine
- Head & Neck Surgery
- Hematology
- Hematopathology
- Hospice & Palliative Medicine
- Hospital Medicine
- Interventional Cardiology
- Interventional Radiology
- Laryngology
- Medical Leadership & Administration
- Medical Microbiology
- Medical Oncology
- Medical Toxicology
- Metabolic & Bariatric Surgery
- Molecular Genetic Pathology
- Musculoskeletal Oncology
- Neonatal-Perinatal Medicine
- Nephrology
- Neuro Anesthesia
- Neurocritical Care
- Neurodevelopmental Disabilities
- Neurological & Spinal Cord Injury Rehab
- Neuromuscular Medicine
- Neuropathology
- Neuroradiology
- Nuclear Medicine
- Obstetric Anesthesia
- Obstetrics & Gynecology
- Ophthalmology
- Orthopaedic Sports Medicine
- Orthopaedic Surgery
- Orthopaedic Trauma
- Otology & Neurotology
- Pain Medicine
- Patient Safety & Quality Improvement
- Pediatric Anesthesia
- Pediatric Cardiology
- Pediatric Critical Care Medicine
- Pediatric Emergency Medicine
- Pediatric Gastroenterology
- Pediatric Hematology-Oncology
- Pediatric Infectious Diseases
- Pediatric Neurology
- Pediatric Orthopaedic Surgery
- Pediatric Otolaryngology
- Pediatric Pathology
- Pediatric Radiology
- Pediatric Rehabilitation Medicine
- Pediatric Surgery
- Pediatric Transplant Hepatology
- Physical Medicine & Rehabilitation
- Practice Management & Ethics
- Primary Care Sports Medicine
- Pulmonary Disease
- Regional Anesthesia & Acute Pain
- Rheumatology
- Rhinology
- Shoulder & Elbow Surgery
- Sleep Medicine
- Spine Surgery
- Surgery of the Hand & Upper Extremity
- Surgical Critical Care
- Surgical Oncology
- Thoracic Anesthesia
- Thoracic Surgery
- Transplant Hepatology
- Transplant Surgery
- Trauma Surgery
- Urology
- Vascular Neurology
- Vascular Surgery
- Anesthesiology
- Cardio-Vascular
- Cross-Specialty
- Emergency & Critical Care
- ENT & Head Neck
- GI & Liver
- Infectious Disease
- Internal Medicine
- Medical Subspecialties
- Neurology
- Ob/Gyn
- Oncology & Hematology
- Orthopedics
- Pain & Palliative
- Pathology & Lab
- Pediatrics
- Primary care
- Radiology
- Rehabilitation
- Sports & Exercise Medicine
- Surgery
- Urology
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